{"id":17050,"date":"2024-03-07T15:05:39","date_gmt":"2024-03-07T18:05:39","guid":{"rendered":"https:\/\/www.grupomedcof.com.br\/blog\/?p=17050"},"modified":"2026-04-24T16:56:24","modified_gmt":"2026-04-24T19:56:24","slug":"cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber","status":"publish","type":"post","link":"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber\/","title":{"rendered":"Cardiopatias cong\u00eanitas cian\u00f3ticas: tudo que voc\u00ea precisa saber"},"content":{"rendered":"<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_74 counter-hierarchy ez-toc-counter ez-toc-transparent ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Sum\u00e1rio<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabela de conte\u00fado\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewBox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewBox=\"0 0 24 24\" version=\"1.2\" baseProfile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 ' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber\/#Epidemiologia\" >Epidemiologia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber\/#Etiologias\" >Etiologias<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber\/#Exames_complementares\" >Exames complementares<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber\/#Achados_extracardiacos\" >Achados extracard\u00edacos<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber\/#Fisiopatologia\" >Fisiopatologia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber\/#Manifestacoes\" >Manifesta\u00e7\u00f5es<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-cianoticas-tudo-o-que-voce-precisa-saber\/#O_metodo_que_te_aprova\" >O m\u00e9todo que te aprova<\/a><\/li><\/ul><\/nav><\/div>\n\n<figure class=\"wp-block-image size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"576\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/03\/1-1-1024x576.jpg\" alt=\"cardiopatias cong\u00eanitas\" class=\"wp-image-21646\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/03\/1-1-1024x576.jpg 1024w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/03\/1-1-300x169.jpg 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/03\/1-1-768x432.jpg 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/03\/1-1-1536x864.jpg 1536w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/03\/1-1.jpg 1920w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><figcaption class=\"wp-element-caption\">cardiopatias cong\u00eanitas<\/figcaption><\/figure>\n\n\n\n<p id=\"h-definicao\"><a href=\"https:\/\/www.grupomedcof.com.br\/blog\/cardiopatias-congenitas-quando-suspeitar-e-como-classificar\/\" target=\"_blank\" rel=\"noreferrer noopener\"><strong>Cardiopatias cong\u00eanitas<\/strong>&nbsp;<\/a>possuem como caracter\u00edsticas os shunts direita-esquerda. Isso significa que h\u00e1 uma mistura de sangue venoso, com baixo teor de oxig\u00eanio, e sangue arterial, com alto teor de oxig\u00eanio, nos sistemas circulat\u00f3rios, o que resulta em cianose perif\u00e9rica.<\/p>\n\n\n\n<figure class=\"wp-block-image size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"320\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/11\/Banner-MedCof-Plus-2200x460-11-1343x420-1-1024x320.png\" alt=\"\" class=\"wp-image-39227\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/11\/Banner-MedCof-Plus-2200x460-11-1343x420-1-1024x320.png 1024w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/11\/Banner-MedCof-Plus-2200x460-11-1343x420-1-300x94.png 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/11\/Banner-MedCof-Plus-2200x460-11-1343x420-1-768x240.png 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/11\/Banner-MedCof-Plus-2200x460-11-1343x420-1-150x47.png 150w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/11\/Banner-MedCof-Plus-2200x460-11-1343x420-1-696x218.png 696w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/11\/Banner-MedCof-Plus-2200x460-11-1343x420-1-1068x334.png 1068w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/11\/Banner-MedCof-Plus-2200x460-11-1343x420-1.png 1343w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-epidemiologia\"><span class=\"ez-toc-section\" id=\"Epidemiologia\"><\/span><strong>Epidemiologia<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>As les\u00f5es card\u00edacas cian\u00f3ticas representam aproximadamente 15% de todos os casos de Doen\u00e7a Card\u00edaca Cong\u00eanita (DCC), e 1\/3 das formas potencialmente fatais de DCC.&nbsp;Al\u00e9m disso, das DCC, a&nbsp;Tetralogia de Fallot&nbsp;\u00e9 a mais frequente, incluindo as acian\u00f3ticas, representando 10% de todas as DCC.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><span class=\"ez-toc-section\" id=\"Etiologias\"><\/span><strong>Etiologias<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Transposi\u00e7\u00e3o de grandes art\u00e9rias (TGA);<\/li>\n\n\n\n<li>Tetralogia de Fallot (T4F);<\/li>\n\n\n\n<li>Dupla via de sa\u00edda do VD com EP;<\/li>\n\n\n\n<li>Ventr\u00edculo \u00fanico com EP;<\/li>\n\n\n\n<li>Atresia pulmonar com septo interventricular \u00edntegro;<\/li>\n\n\n\n<li>Tronco arterioso;<\/li>\n\n\n\n<li>Drenagem an\u00f4mala total das veias pulmonares;<\/li>\n\n\n\n<li>Atresia tric\u00faspide;<\/li>\n\n\n\n<li>Anomalia de Ebstein;<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-exames-complementares\"><span class=\"ez-toc-section\" id=\"Exames_complementares\"><\/span><strong>Exames complementares<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Exames de imagem, como a&nbsp;radiografia de t\u00f3rax,&nbsp;podem fornecer informa\u00e7\u00f5es importantes sobre a anatomia card\u00edaca e pulmonar. Em cardiopatias cong\u00eanitas cian\u00f3ticas, \u00e9 poss\u00edvel observar um cora\u00e7\u00e3o aumentado em certas \u00e1reas e uma \u201cbota\u201d ou \u201carranjo em arranha-c\u00e9u\u201d, aumento da trama pulmonar de forma assim\u00e9trica na radiografia, indicando m\u00e1 circula\u00e7\u00e3o sangu\u00ednea.&nbsp;<\/p>\n\n\n\n<p>Quanto ao&nbsp;eletrocardiograma, pode revelar ritmos anormais, hipertrofia ventricular direita ou sobrecarga atrial<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-achados-extracardiacos\"><span class=\"ez-toc-section\" id=\"Achados_extracardiacos\"><\/span><strong>Achados extracard\u00edacos<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Algumas cardiopatias cong\u00eanitas cian\u00f3ticas podem apresentar achados extracard\u00edacos significativos, seja por associa\u00e7\u00e3o de uma s\u00edndrome gen\u00e9tica, seja por altera\u00e7\u00f5es sobrepostas.<\/p>\n\n\n\n<p>Por exemplo, os pacientes com a S\u00edndrome de Eisenmenger podem exibir caracter\u00edsticas como hipertrofia das extremidades, baqueteamento digital e cianose central.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-fisiopatologia\"><span class=\"ez-toc-section\" id=\"Fisiopatologia\"><\/span><strong>Fisiopatologia<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Por ser uma cardiopatia por o shunt direita- esquerda e, portanto, podem ser subdivididas em categorias fisiopatol\u00f3gicas:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Diminui\u00e7\u00e3o do fluxo sangu\u00edneo pulmonar:<\/strong>\u00a0caracterizado por\u00a0<strong>hipofluxo,<\/strong>\u00a0devido ao sequestro de volume;<\/li>\n\n\n\n<li><span style=\"color: initial;\">Tetralogia de Fallot;Atresia pulmonar com seto interventricular \u00edntegro;Estenose pulmonar cr\u00edtica;<\/span><\/li>\n\n\n\n<li><strong>Aumento do fluxo sangu\u00edneo pulmonar:<\/strong>\u00a0com uma conex\u00e3o ventr\u00edculo-arterial discordante, como a transposi\u00e7\u00e3o de grandes vasos<\/li>\n\n\n\n<li><strong>Les\u00e3o obstrutiva esquerda<\/strong>\u00a0com shunt da direita para a esquerda, como a s\u00edndrome do cora\u00e7\u00e3o esquerdo hipopl\u00e1sico e coarcta\u00e7\u00e3o de aorta;<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-manifestacoes\"><span class=\"ez-toc-section\" id=\"Manifestacoes\"><\/span><strong>Manifesta\u00e7\u00f5es<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<h4 class=\"wp-block-heading\" id=\"h-historia-clinica\"><strong>Hist\u00f3ria Cl\u00ednica<\/strong><\/h4>\n\n\n\n<p>Uma hist\u00f3ria cl\u00ednica minuciosa \u00e9 a base para suspeitar de uma cardiopatia cong\u00eanita cian\u00f3tica. Pais ou cuidadores podem relatar sintomas como cianose (\u201do beb\u00ea ficou roxinho\u201d), dificuldades respirat\u00f3rias, cansa\u00e7o e\/ou sudorese durante a alimenta\u00e7\u00e3o, desmaios, atraso no desenvolvimento ou incapacidade de ganhar peso. Al\u00e9m disso, importante questionar a&nbsp;<strong>presen\u00e7a de DCC na fam\u00edlia.<\/strong><\/p>\n\n\n\n<h4 class=\"wp-block-heading\" id=\"h-exame-fisico\"><strong>Exame F\u00edsico<\/strong><\/h4>\n\n\n\n<p>A presen\u00e7a de cianose, especialmente nas extremidades e nos l\u00e1bios, \u00e9 um sinal marcante. Al\u00e9m disso, observar o ritmo e a frequ\u00eancia card\u00edaca, auscultar sopros card\u00edacos e avaliar a qualidade dos pulsos arteriais s\u00e3o componentes essenciais do exame.<\/p>\n\n\n\n<p>Os achados do exame f\u00edsico diferem dependendo de cada uma das cardiopatias.<\/p>\n\n\n\n<p>Ademais, a hepatomegalia ocorre mais comumente em pacientes que evoluem com insufici\u00eancia card\u00edaca devido a les\u00f5es obstrutivas do lado esquerdo.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-o-metodo-que-te-aprova\"><span class=\"ez-toc-section\" id=\"O_metodo_que_te_aprova\"><\/span><strong>O m\u00e9todo que te aprova<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Se voc\u00ea quer garantir a sua aprova\u00e7\u00e3o nas provas de resid\u00eancia, ent\u00e3o conhe\u00e7a o\u00a0<strong>Grupo MedCof\u00a0<\/strong>e a metodologia que j\u00e1 aprovou<strong><a href=\"https:\/\/www.grupomedcof.com.br\/blog\/presenca-da-medcof-nas-aprovacoes-em-residencia-medica-no-brasil\/\">\u00a0mais de 35 mil<\/a>\u00a0<\/strong>residentes pelo pa\u00eds. Confira abaixo o nosso\u00a0<a href=\"https:\/\/youtu.be\/gUlaCvEroV0?si=bfad6fh76cg9iAFR\"><strong>COFEXPRESS<\/strong><\/a>\u00a0sobre o assunto:<\/p>\n\n\n\n<figure class=\"wp-block-embed is-provider-youtube wp-block-embed-youtube\"><div class=\"wp-block-embed__wrapper\">\n<iframe loading=\"lazy\" title=\"Saiu da faculdade e j\u00e1 estava aprovada: Entenda o m\u00e9todo por tr\u00e1s | #PapoDeAprovado Ep13\" width=\"696\" height=\"392\" src=\"https:\/\/www.youtube.com\/embed\/2O8zZ55sk5U?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe>\n<\/div><\/figure>\n\n\n","protected":false},"excerpt":{"rendered":"<p>As cardiopatias cong\u00eanitas cian\u00f3ticas s\u00e3o caracterizadas por shunts direita-esquerda, o que significa que h\u00e1 uma mistura de sangue venoso &#8230;<\/p>\n","protected":false},"author":10,"featured_media":21646,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[211,120],"tags":[154,169,109,117,68],"ppma_author":[3613],"class_list":{"0":"post-17050","1":"post","2":"type-post","3":"status-publish","4":"format-standard","5":"has-post-thumbnail","7":"category-cardiologia","8":"category-pediatria","9":"tag-cardiologia","10":"tag-cardiologia-pediatrica","11":"tag-pediatria","12":"tag-provas-de-residencia","13":"tag-residencia-medica"},"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v24.3 (Yoast SEO v27.4) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Cardiopatias Cong\u00eanitas Cian\u00f3ticas: Guia Completo | Medcof<\/title>\n<meta name=\"description\" content=\"As cardiopatias cong\u00eanitas cian\u00f3ticas s\u00e3o caracterizadas por shunts direita-esquerda, o que significa que h\u00e1 uma 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