{"id":33611,"date":"2025-02-13T15:21:16","date_gmt":"2025-02-13T18:21:16","guid":{"rendered":"https:\/\/www.grupomedcof.com.br\/blog\/?p=33611"},"modified":"2026-04-27T09:50:39","modified_gmt":"2026-04-27T12:50:39","slug":"sindrome-de-sjogren","status":"publish","type":"post","link":"https:\/\/www.grupomedcof.com.br\/blog\/sindrome-de-sjogren\/","title":{"rendered":"S\u00edndrome de Sj\u00f6gren: entenda mais sobre essa doen\u00e7a autoimune!"},"content":{"rendered":"<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_74 counter-hierarchy ez-toc-counter ez-toc-transparent ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Sum\u00e1rio<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabela de conte\u00fado\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewBox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewBox=\"0 0 24 24\" version=\"1.2\" baseProfile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 ' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/sindrome-de-sjogren\/#Como_ela_se_manifesta\" >Como ela se manifesta?<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/sindrome-de-sjogren\/#Exocrinopatia\" >Exocrinopatia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/sindrome-de-sjogren\/#Manifestacoes_Extraglandulares\" >Manifesta\u00e7\u00f5es Extraglandulares<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/sindrome-de-sjogren\/#Como_diagnosticamos\" >Como diagnosticamos?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/sindrome-de-sjogren\/#E_como_fazer_o_tratamento\" >E como fazer o tratamento?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/sindrome-de-sjogren\/#Quais_as_complicacoes\" >Quais as complica\u00e7\u00f5es?&nbsp;<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/sindrome-de-sjogren\/#O_metodo_que_te_aprova\" >O m\u00e9todo que te aprova!<\/a><\/li><\/ul><\/nav><\/div>\n\n<figure class=\"wp-block-image size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"576\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-1024x576.jpg\" alt=\"Sindrome de Sj\u00f6gren\u00a0\" class=\"wp-image-33613\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-1024x576.jpg 1024w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-300x169.jpg 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-768x432.jpg 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-1536x864.jpg 1536w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-747x420.jpg 747w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-150x84.jpg 150w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-696x392.jpg 696w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81-1068x601.jpg 1068w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-81.jpg 1920w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n\n\n\n<p>A <strong>Sindrome de Sj\u00f6gren <\/strong>\u00e9 uma doen\u00e7a autoimune cr\u00f4nica, caracterizada pela infiltra\u00e7\u00e3o linfocit\u00e1ria das gl\u00e2ndulas ex\u00f3crinas, levando a sintomas de secura, como xeroftalmia e xerostomia. Essa condi\u00e7\u00e3o\u00a0 \u00e9 frequentemente referida como a &#8220;doen\u00e7a seca&#8221; devido aos seus sintomas predominantes de secura. Ela afeta principalmente mulheres de meia-idade, com uma propor\u00e7\u00e3o de 10:1 em rela\u00e7\u00e3o aos homens. A doen\u00e7a pode ocorrer isoladamente ou em associa\u00e7\u00e3o com outras doen\u00e7as autoimunes, como l\u00fapus eritematoso sist\u00eamico (LES) e artrite reumatoide.<\/p>\n\n\n\n<figure class=\"wp-block-image is-resized\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXcixffuw7-RzXwCuO6xmZAXluO0qsm37Zzet6usyU1duR_pdMWo3iX-IseEPqKaiFAIVYzICGxrq97GIze-dHb59pfeUeEb3rzBNlOFfXZ05It4eklqk-3uJHg--aV-LwrzOu6s?key=BPMaqcohHuM0t-NDgkeZMBLE\" alt=\"Sindrome de Sj\u00f6gren\u00a0\" style=\"width:541px;height:auto\"\/><figcaption class=\"wp-element-caption\">Paciente com parotidite. Fonte: American College of Rheumatology.&nbsp;<\/figcaption><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-como-ela-se-manifesta\"><span class=\"ez-toc-section\" id=\"Como_ela_se_manifesta\"><\/span><strong>Como ela se manifesta?<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-exocrinopatia\"><span class=\"ez-toc-section\" id=\"Exocrinopatia\"><\/span><strong>Exocrinopatia<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>A exocrinopatia \u00e9 a caracter\u00edstica mais comum, presente em 60% dos casos, e inclui:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Xeroftalmia: Secura ocular que pode causar ardor, dor e prurido.<\/li>\n\n\n\n<li>Xerostomia: Secura bucal que leva a dificuldades na mastiga\u00e7\u00e3o, altera\u00e7\u00e3o do paladar e aumento do risco de c\u00e1ries.<\/li>\n<\/ul>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXfInxS8EsPyMAHMadz1r1NlOVK18SpxuVHpTccyncI_sNABmsDimL1YV3yX6nymtEr43h1d5_KoEmzxmlk0gnmfP4MkPxch25Vw2SNxFXmLdCp6rrl8HES3LKYYOtbVeK6KKHAeFQ?key=BPMaqcohHuM0t-NDgkeZMBLE\" alt=\"Sindrome de Sj\u00f6gren\u00a0\"\/><figcaption class=\"wp-element-caption\">Xerostomia. Fonte: American College of Rheumatology.<\/figcaption><\/figure>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-manifestacoes-extraglandulares\"><span class=\"ez-toc-section\" id=\"Manifestacoes_Extraglandulares\"><\/span><strong>Manifesta\u00e7\u00f5es Extraglandulares<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Em 40% dos casos, a s\u00edndrome apresenta manifesta\u00e7\u00f5es extraglandulares, afetando m\u00faltiplos sistemas:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Articular: Poliartrite sim\u00e9trica, semelhante \u00e0 artralgia no LES, predominando em pequenas articula\u00e7\u00f5es.<\/li>\n\n\n\n<li>Pulmonar: Intersticiopatia com padr\u00e3o linfoc\u00edtico, incluindo Pneumonia Intersticial N\u00e3o Espec\u00edfica (PINE) e pneumonite linfoc\u00edtica intersticial.<\/li>\n\n\n\n<li>Hematol\u00f3gico: Leucopenia, plaquetopenia e anemia hemol\u00edtica.<\/li>\n\n\n\n<li>Neurol\u00f3gico: Comprometimento do sistema nervoso perif\u00e9rico, apresentando-se como neuropatia sensitiva ou motora.<\/li>\n\n\n\n<li>Cut\u00e2neo: Xerose cut\u00e2nea, vasculite e p\u00farpura nos membros inferiores.<\/li>\n<\/ul>\n\n\n\n<figure class=\"wp-block-image is-resized\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXexf32KSPB60rg8oUuoUsKMnP1oswS36CLuYYEe7NhFSc40S7Os-Tl0Evj9HbchYIugRbRzomDzdFBmduIpyQ6qtqDSgHlsMjvVOSSH6PE9SBnf5IPKu1Nh4TamEQVh5pAEi3CJqA?key=BPMaqcohHuM0t-NDgkeZMBLE\" alt=\"Sindrome de Sj\u00f6gren\u00a0\" style=\"width:578px;height:auto\"\/><figcaption class=\"wp-element-caption\">Padr\u00e3o de Penumonite linfoc\u00edtica intersticial. Fonte: Radiopaedia<\/figcaption><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-como-diagnosticamos\"><span class=\"ez-toc-section\" id=\"Como_diagnosticamos\"><\/span><strong>Como diagnosticamos?<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>O diagn\u00f3stico da S\u00edndrome de Sj\u00f6gren \u00e9 baseado em crit\u00e9rios cl\u00ednicos e laboratoriais, incluindo:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Anticorpos: Presen\u00e7a de Anti-Ro (30-60%) e Anti-La (15-40%), al\u00e9m de FAN e fator reumatoide.<\/li>\n\n\n\n<li>Teste de Schirmer: Considerado positivo quando a umidade ocular \u00e9 inferior a 5 mm em 5 minutos.<\/li>\n\n\n\n<li>Bi\u00f3psia de gl\u00e2ndula salivar: Demonstra infiltra\u00e7\u00e3o linfocit\u00e1ria focal.<\/li>\n<\/ul>\n\n\n\n<p>Os crit\u00e9rios classificat\u00f3rios ACR\/EULAR 2016 s\u00e3o frequentemente utilizados, exigindo \u2265 4 pontos para o diagn\u00f3stico.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXehmR5_JLet5hSffs16dC_-dPASfVDDI1AM19wmL6yxv-GzM61oBK_HuULIpO_vrB0c68ruQ0Q0poiEAFUNuS1an5qKQkhdFpw8dSinlXzGbfWQ_qDPs1BEVGkyT1LrhWHHdbXwpg?key=BPMaqcohHuM0t-NDgkeZMBLE\" alt=\"Sindrome de Sj\u00f6gren\u00a0\"\/><figcaption class=\"wp-element-caption\">Fonte: <a href=\"https:\/\/doi.org\/10.1590\/S0482-50042010000500001\">https:\/\/doi.org\/10.1590\/S0482-50042010000500001<\/a>&nbsp;<\/figcaption><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-e-como-fazer-o-tratamento\"><span class=\"ez-toc-section\" id=\"E_como_fazer_o_tratamento\"><\/span><strong>E como fazer o tratamento?<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Podemos seguir uma abordagem n\u00e3o farmacol\u00f3gica com:&nbsp;<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Prote\u00e7\u00e3o Ocular: Uso de \u00f3culos de prote\u00e7\u00e3o e l\u00e1grimas artificiais.<\/li>\n\n\n\n<li>Hidrata\u00e7\u00e3o Oral: Uso de saliva artificial e chicletes sem a\u00e7\u00facar.<\/li>\n\n\n\n<li>Modifica\u00e7\u00f5es Ambientais: Uso de umidificadores e evitar medicamentos que pioram a secura.<\/li>\n<\/ul>\n\n\n\n<p>Ou, dependendo do caso, seguimos com o tratamento farmacol\u00f3gico:&nbsp;<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Secretagogos: Pilocarpina para estimular a produ\u00e7\u00e3o de saliva e l\u00e1grimas.<\/li>\n\n\n\n<li>Imunomoduladores: Hidroxicloroquina para benef\u00edcio imunomodulador.<\/li>\n\n\n\n<li>Imunossupressores: Em casos graves, o uso de rituximabe pode ser considerado para deple\u00e7\u00e3o de linf\u00f3citos B.<\/li>\n<\/ul>\n\n\n\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/www.grupomedcof.com.br\/cofletters\/\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"366\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1024x366.png\" alt=\"\" class=\"wp-image-30896\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1024x366.png 1024w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-300x107.png 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-768x275.png 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1536x549.png 1536w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-2048x732.png 2048w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1175x420.png 1175w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-150x54.png 150w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-696x249.png 696w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1068x382.png 1068w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1920x686.png 1920w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><\/a><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-quais-as-complicacoes\"><span class=\"ez-toc-section\" id=\"Quais_as_complicacoes\"><\/span><strong>Quais as complica\u00e7\u00f5es?&nbsp;<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>A complica\u00e7\u00e3o mais grave associada \u00e0 S\u00edndrome de Sj\u00f6gren \u00e9 o desenvolvimento de linfoma, especialmente em pacientes com aumento persistente das par\u00f3tidas, linfadenopatia, p\u00farpura e consumo de complemento. A vigil\u00e2ncia cont\u00ednua \u00e9 essencial para a detec\u00e7\u00e3o precoce e manejo adequado.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"o-m\u00e9todo-que-te-aprova\"><span class=\"ez-toc-section\" id=\"O_metodo_que_te_aprova\"><\/span><strong>O m\u00e9todo que te aprova!<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Quer alcan\u00e7ar a aprova\u00e7\u00e3o nas provas de resid\u00eancia m\u00e9dica? Ent\u00e3o seja um&nbsp;<a href=\"https:\/\/www.grupomedcof.com.br\/home\/\" target=\"_blank\" rel=\"noreferrer noopener\"><strong>MedCoffer<\/strong><\/a>! Aqui, te ajudaremos na busca da aprova\u00e7\u00e3o com conte\u00fados de qualidade e uma&nbsp;<a href=\"https:\/\/www.grupomedcof.com.br\/blog\/presenca-da-medcof-nas-aprovacoes-em-residencia-medica-no-brasil\/\" target=\"_blank\" rel=\"noreferrer noopener\"><strong>metodologia que j\u00e1 aprovou mais de 10 mil residentes no pa\u00eds<\/strong><\/a>! Por fim, acesse o nosso<a href=\"https:\/\/www.youtube.com\/@GrupoMedcof\/featured\" target=\"_blank\" rel=\"noreferrer noopener\">&nbsp;<strong>canal do youtube&nbsp;<\/strong><\/a>para ver o nosso material.<\/p>\n\n\n\n<figure class=\"wp-block-embed is-type-video is-provider-youtube wp-block-embed-youtube wp-embed-aspect-16-9 wp-has-aspect-ratio\"><div class=\"wp-block-embed__wrapper\">\n<div class=\"youtube-embed\" data-video_id=\"VewEBMjnsMM\"><iframe loading=\"lazy\" title=\"Resid\u00eancia M\u00e9dica na UNICAMP: Aprovado em R1 Anestesiologia\" width=\"696\" height=\"392\" src=\"https:\/\/www.youtube.com\/embed\/VewEBMjnsMM?feature=oembed&#038;enablejsapi=1\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe><\/div>\n<\/div><\/figure>\n","protected":false},"excerpt":{"rendered":"<p>A S\u00edndrome de Sj\u00f6gren \u00e9 uma doen\u00e7a autoimune cr\u00f4nica, caracterizada pela infiltra\u00e7\u00e3o linfocit\u00e1ria das gl\u00e2ndulas ex\u00f3crinas. Entenda mais!<\/p>\n","protected":false},"author":21,"featured_media":33613,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[115],"tags":[2577,2578,2576],"ppma_author":[3617],"class_list":{"0":"post-33611","1":"post","2":"type-post","3":"status-publish","4":"format-standard","5":"has-post-thumbnail","7":"category-clinica-medica","8":"tag-exocrinopatia","9":"tag-manifestacoes-extraglandulares","10":"tag-sindrome-de-sjogren"},"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v24.3 (Yoast SEO v27.5) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>S\u00edndrome de Sj\u00f6gren: Entenda a Doen\u00e7a Autoimune | Medcof<\/title>\n<meta name=\"description\" content=\"A Sindrome de Sj\u00f6gren \u00e9 uma doen\u00e7a autoimune cr\u00f4nica, caracterizada pela infiltra\u00e7\u00e3o linfocit\u00e1ria das gl\u00e2ndulas ex\u00f3crinas. 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