{"id":33633,"date":"2025-02-14T16:34:48","date_gmt":"2025-02-14T19:34:48","guid":{"rendered":"https:\/\/www.grupomedcof.com.br\/blog\/?p=33633"},"modified":"2025-02-14T16:34:49","modified_gmt":"2025-02-14T19:34:49","slug":"doencas-desmielinizantes-a-fisiopatologia-envolvida","status":"publish","type":"post","link":"https:\/\/www.grupomedcof.com.br\/blog\/doencas-desmielinizantes-a-fisiopatologia-envolvida\/","title":{"rendered":"Doen\u00e7as desmielinizantes: a fisiopatologia envolvida\u00a0"},"content":{"rendered":"<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_74 counter-hierarchy ez-toc-counter ez-toc-transparent ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Sum\u00e1rio<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabela de conte\u00fado\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewBox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewBox=\"0 0 24 24\" version=\"1.2\" baseProfile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 ' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/doencas-desmielinizantes-a-fisiopatologia-envolvida\/#Esclerose_Multipla_EM\" >Esclerose M\u00faltipla (EM)<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/doencas-desmielinizantes-a-fisiopatologia-envolvida\/#Encefalomielite_Disseminada_Aguda_ADEM\" >Encefalomielite Disseminada Aguda (ADEM)<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/doencas-desmielinizantes-a-fisiopatologia-envolvida\/#Doenca_do_Espectro_da_Neuromielite_Optica_NMOSD\" >Doen\u00e7a do Espectro da Neuromielite \u00d3ptica (NMOSD)<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/doencas-desmielinizantes-a-fisiopatologia-envolvida\/#Sindromes_Associadas_a_Anticorpos_Anti-MOG_MOGAD\" >S\u00edndromes Associadas a Anticorpos Anti-MOG (MOGAD)<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/doencas-desmielinizantes-a-fisiopatologia-envolvida\/#Encefalites_Autoimunes_na_Infancia\" >Encefalites Autoimunes na Inf\u00e2ncia<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/doencas-desmielinizantes-a-fisiopatologia-envolvida\/#Seja_um_MedCofer\" >Seja um MedCofer!<\/a><\/li><\/ul><\/nav><\/div>\n\n<figure class=\"wp-block-image size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"576\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-1024x576.jpg\" alt=\"\" class=\"wp-image-33634\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-1024x576.jpg 1024w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-300x169.jpg 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-768x432.jpg 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-1536x864.jpg 1536w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-747x420.jpg 747w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-150x84.jpg 150w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-696x392.jpg 696w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83-1068x601.jpg 1068w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/02\/Blog-MedCof-83.jpg 1680w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n\n\n\n<p>As <strong>doen\u00e7as desmielinizantes<\/strong> e a encefalite autoimune constituem um campo complexo e fascinante da neuroimunologia pedi\u00e1trica. Com os avan\u00e7os recentes, \u00e9 essencial que residentes em medicina compreendam as nuances dessas condi\u00e7\u00f5es para um diagn\u00f3stico e tratamento eficazes.<\/p>\n\n\n\n<p>As doen\u00e7as desmielinizantes s\u00e3o caracterizadas pela perda da bainha de mielina que envolve as fibras nervosas, resultando em comprometimento da condu\u00e7\u00e3o nervosa. Entre as principais condi\u00e7\u00f5es, destacam-se a Esclerose M\u00faltipla (EM), a Encefalomielite Disseminada Aguda (ADEM) e a Doen\u00e7a do Espectro da Neuromielite \u00d3ptica (NMOSD).<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-esclerose-multipla-em\"><span class=\"ez-toc-section\" id=\"Esclerose_Multipla_EM\"><\/span><strong>Esclerose M\u00faltipla (EM)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>A EM \u00e9 uma doen\u00e7a inflamat\u00f3ria e neurodegenerativa que afeta predominantemente a subst\u00e2ncia branca e cinzenta do sistema nervoso central (SNC). Embora mais comum em adultos, cerca de 3-5% dos casos surgem antes dos 18 anos. A doen\u00e7a \u00e9 mais prevalente em mulheres, especialmente ap\u00f3s a puberdade.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXfBOiEL1LgNIDsKn0T6zb4d4FsKtVmX7P3ExI6h4rYacI5ObFUx4OUAQX_KFSjEHRdDMEKHfh5mhdAz_6ItITKROqnqXvX51hx1eRmC4PY23SWGucdDUNhFN2zoSWXLWV2DsPOtnA?key=lSpQPo-ycysl0znIiFQKSO5j\" alt=\"\"\/><figcaption class=\"wp-element-caption\">Fonte: <a href=\"https:\/\/pin.it\/57UoUGsbd\">https:\/\/pin.it\/57UoUGsbd<\/a>\u00a0<\/figcaption><\/figure>\n\n\n\n<p>&nbsp;A forma remitente-recorrente \u00e9 a mais comum, caracterizada por surtos de piora neurol\u00f3gica seguidos de recupera\u00e7\u00e3o parcial ou completa. O diagn\u00f3stico dessa condi\u00e7\u00e3o se baseia nos crit\u00e9rios de McDonald, que incluem evid\u00eancias de dissemina\u00e7\u00e3o no espa\u00e7o e no tempo.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXedDgNij4fsQU_cQzk07Md32wkdAt9vAK7Mx-Rfy8wLvyzvgkkcAVVc_CAc8i5q0qqOjHP3UGZ0Kxz5CAoaRA0MD7dqq9wCXz5l1jMovesd-PEYuDxuYDm6egKyBoc9ZpSVhHh5sg?key=lSpQPo-ycysl0znIiFQKSO5j\" alt=\"\"\/><figcaption class=\"wp-element-caption\">Fonte: <a href=\"https:\/\/pedrorpb.blogspot.com\/2012\/08\/\">https:\/\/pedrorpb.blogspot.com\/2012\/08\/<\/a>\u00a0<\/figcaption><\/figure>\n\n\n\n<p>O tratamento inclui corticoster\u00f3ides para surtos agudos e imunoterapia cr\u00f4nica para casos recorrentes.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-encefalomielite-disseminada-aguda-adem\"><span class=\"ez-toc-section\" id=\"Encefalomielite_Disseminada_Aguda_ADEM\"><\/span><strong>Encefalomielite Disseminada Aguda (ADEM)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>A ADEM \u00e9 mais prevalente em crian\u00e7as, com uma idade m\u00e9dia de acometimento entre 5-8 anos. A condi\u00e7\u00e3o geralmente segue infec\u00e7\u00f5es respirat\u00f3rias ou vacina\u00e7\u00e3o.<\/p>\n\n\n\n<p>Ela se manifesta com d\u00e9ficits neurol\u00f3gicos multifocais, como ataxia e crises epil\u00e9pticas.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXc71h15pxPnkAc2D7RkgIT1ZXuGRzvPJwDuqe77q1KTGjygemh530j-kN15fAcDc2HOr_y7aVFxVw9ssBlzlpXlXm1Ieu-ELm8Wyug4la-HvuIGO7Zmw9CdimJ5w4mpEOS3XDWfAw?key=lSpQPo-ycysl0znIiFQKSO5j\" alt=\"\"\/><figcaption class=\"wp-element-caption\">Fonte: <a href=\"https:\/\/www.scielo.br\/j\/rbof\/a\/VY5Q6qsqHkCBLnhcLNpsytS\/\">https:\/\/www.scielo.br\/j\/rbof\/a\/VY5Q6qsqHkCBLnhcLNpsytS\/<\/a>\u00a0<\/figcaption><\/figure>\n\n\n\n<p>O diagn\u00f3stico requer a presen\u00e7a de um evento cl\u00ednico multifocal do SNC, acompanhado de altera\u00e7\u00f5es em exames de imagem. Por fim, a primeira linha de tratamento envolve corticosteroides intravenosos, seguidos de terapia imunomoduladora.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-doenca-do-espectro-da-neuromielite-optica-nmosd\"><span class=\"ez-toc-section\" id=\"Doenca_do_Espectro_da_Neuromielite_Optica_NMOSD\"><\/span><strong>Doen\u00e7a do Espectro da Neuromielite \u00d3ptica (NMOSD)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>A NMOSD \u00e9 uma astrocitopatia auto imune prim\u00e1ria com desmieliniza\u00e7\u00e3o secund\u00e1ria. \u00c9 mais comum em mulheres n\u00e3o-brancas, com apresenta\u00e7\u00e3o t\u00edpica por volta dos 30-40 anos.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXcyJWk-AIMktBA-GJ7wClkAKHySf2uS8WxK8rAQdDpx5loOWoJC67x4SajJnbpvpX9WnncK997cZ08ZyfPjqgTT6hF3S13ttyK6i6ohU43R5_VYWOL6YS7lH2LPHvMWZFykwr4s?key=lSpQPo-ycysl0znIiFQKSO5j\" alt=\"\"\/><figcaption class=\"wp-element-caption\">Fonte: <a href=\"https:\/\/images.app.goo.gl\/WvkySD3sfedhkvw89\">https:\/\/images.app.goo.gl\/WvkySD3sfedhkvw89<\/a>\u00a0<\/figcaption><\/figure>\n\n\n\n<p>As manifesta\u00e7\u00f5es cl\u00ednicas incluem ataques de neurite \u00f3ptica e mielite transversa longitudinalmente extensa. Baseamos o diagn\u00f3stico na presen\u00e7a de anticorpos anti-AQP4 e caracter\u00edsticas cl\u00ednicas t\u00edpicas. Finalizando, sabemos que o tratamento envolve corticosteroides e imunoterapia, com necessidade de tratamento cr\u00f4nico.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-sindromes-associadas-a-anticorpos-anti-mog-mogad\"><span class=\"ez-toc-section\" id=\"Sindromes_Associadas_a_Anticorpos_Anti-MOG_MOGAD\"><\/span><strong>S\u00edndromes Associadas a Anticorpos Anti-MOG (MOGAD)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Os anticorpos anti-MOG s\u00e3o mais frequentes na popula\u00e7\u00e3o pedi\u00e1trica e est\u00e3o associados a diferentes fen\u00f3tipos cl\u00ednicos, como ADEM e neurite \u00f3ptica recorrente. Nela reconhecemos neurite \u00f3ptica e mielite transversa como mais comuns, frequentemente com evolu\u00e7\u00e3o monof\u00e1sica. O diagn\u00f3stico requer a presen\u00e7a de anticorpos anti-MOG no soro, juntamente com manifesta\u00e7\u00f5es cl\u00ednicas espec\u00edficas. J\u00e1 o tratamento inclui corticosteroides, imunoglobulina e plasmaf\u00e9rese.<\/p>\n\n\n\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/www.grupomedcof.com.br\/cofletters\/\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"366\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1024x366.png\" alt=\"\" class=\"wp-image-30896\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1024x366.png 1024w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-300x107.png 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-768x275.png 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1536x549.png 1536w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-2048x732.png 2048w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1175x420.png 1175w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-150x54.png 150w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-696x249.png 696w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1068x382.png 1068w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2024\/10\/Capa-Eventos-MedCof-Plus-1-1920x686.png 1920w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><\/a><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-encefalites-autoimunes-na-infancia\"><span class=\"ez-toc-section\" id=\"Encefalites_Autoimunes_na_Infancia\"><\/span><strong>Encefalites Autoimunes na Inf\u00e2ncia<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>As encefalites autoimunes s\u00e3o caracterizadas por sintomas neuropsiqui\u00e1tricos associados a anticorpos antineuronais. A encefalite por anticorpos anti-NMDAr \u00e9 a mais comum na inf\u00e2ncia.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXfRfOt_BsBdH6TwPcmAPIelhKyunVzGx1HyYzkQeMc2me-dwOSmNkyrOtm13JqgrYGXs5V0Pj6e0Qy7Snyd32FWoJh3TsL9tEmPST3BjrS95s3OjGWG3BUMQCuD2sBSrYS5sUYPfw?key=lSpQPo-ycysl0znIiFQKSO5j\" alt=\"\"\/><figcaption class=\"wp-element-caption\">Fonte: <a href=\"https:\/\/images.app.goo.gl\/Uiwpwer3yEeC7hgA9\">https:\/\/images.app.goo.gl\/Uiwpwer3yEeC7hgA9<\/a>\u00a0<\/figcaption><\/figure>\n\n\n\n<p>Podemos identificar sintomas psiqui\u00e1tricos, crises epil\u00e9pticas e disautonomia. Conseguimos diagnosticar por meio de exames de imagem, an\u00e1lise do l\u00edquor e painel de autoanticorpos. O tratamento envolve corticosteroides, imunoglobulina e, em alguns casos, ressec\u00e7\u00e3o tumoral.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"seja-um-medcofer\"><span class=\"ez-toc-section\" id=\"Seja_um_MedCofer\"><\/span><strong>Seja um MedCofer!<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Quer alcan\u00e7ar a aprova\u00e7\u00e3o nas provas de resid\u00eancia m\u00e9dica? Ent\u00e3o seja um&nbsp;<a href=\"https:\/\/www.grupomedcof.com.br\/home\/\"><strong>MedCoffer<\/strong><\/a>! Aqui te ajudaremos na busca da aprova\u00e7\u00e3o com conte\u00fados de qualidade e uma metodologia que j\u00e1 aprovou mais de 10 mil residentes no pa\u00eds! Por fim, acesse o nosso<a href=\"https:\/\/www.youtube.com\/@GrupoMedcof\/featured\">&nbsp;<strong>canal do youtube&nbsp;<\/strong><\/a>para ver o nosso material.<\/p>\n\n\n\n<figure class=\"wp-block-embed is-type-video is-provider-youtube wp-block-embed-youtube wp-embed-aspect-16-9 wp-has-aspect-ratio\"><div class=\"wp-block-embed__wrapper\">\n<div class=\"youtube-embed\" data-video_id=\"CqXGCGqt2C4\"><iframe loading=\"lazy\" title=\"COFEXPRESS - Doen\u00e7as Desmielinizantes e Encefalite Autoimune. Com Dr. Joemir Brito\" width=\"696\" height=\"392\" src=\"https:\/\/www.youtube.com\/embed\/CqXGCGqt2C4?feature=oembed&#038;enablejsapi=1\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe><\/div>\n<\/div><\/figure>\n","protected":false},"excerpt":{"rendered":"<p>As doen\u00e7as desmielinizantes e a encefalite autoimune constituem um campo complexo e fascinante da neuroimunologia pedi\u00e1trica. 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