{"id":36971,"date":"2025-08-11T08:01:31","date_gmt":"2025-08-11T11:01:31","guid":{"rendered":"https:\/\/www.grupomedcof.com.br\/blog\/?p=36971"},"modified":"2025-08-11T08:01:33","modified_gmt":"2025-08-11T11:01:33","slug":"saiba-quais-disturbios-envolvem-as-vasculites-sistemicas","status":"publish","type":"post","link":"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/","title":{"rendered":"Saiba quais dist\u00farbios envolvem as Vasculites Sist\u00eamicas"},"content":{"rendered":"<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_74 counter-hierarchy ez-toc-counter ez-toc-transparent ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Sum\u00e1rio<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Alternar tabela de conte\u00fado\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #999;color:#999\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewBox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #999;color:#999\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewBox=\"0 0 24 24\" version=\"1.2\" baseProfile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 ' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#O_que_e_vasculite\" >O que \u00e9 vasculite?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Vasculites_de_Grandes_Vasos\" >Vasculites de Grandes Vasos<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Arterite_de_Celulas_Gigantes_ACG\" >Arterite de C\u00e9lulas Gigantes (ACG)<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Vasculites_de_Medios_Vasos\" >Vasculites de M\u00e9dios Vasos<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Poliarterite_Nodosa_PAN\" >Poliarterite Nodosa (PAN)<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Vasculites_de_Pequenos_Vasos\" >Vasculites de Pequenos Vasos<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Vasculites_ANCA-associadas\" >Vasculites ANCA-associadas<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-8\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Granulomatose_com_Poliangiite_GPA\" >Granulomatose com Poliangiite (GPA)<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-9\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Granulomatose_Eosinofilica_com_Poliangiite_GEPA\" >Granulomatose Eosinof\u00edlica com Poliangiite (GEPA)<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-10\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Poliangiite_Microscopica_PAM\" >Poliangiite Microsc\u00f3pica (PAM)<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-11\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#Crioglobulinemia\" >Crioglobulinemia<\/a><\/li><\/ul><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-12\" href=\"https:\/\/www.grupomedcof.com.br\/blog\/saiba-quais-disturbios-envolvem-as-vasculites-sistemicas\/#O_metodo_que_te_aprova\" >O m\u00e9todo que te aprova!<\/a><\/li><\/ul><\/nav><\/div>\n\n<figure class=\"wp-block-image size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"576\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-1024x576.jpg\" alt=\"\" class=\"wp-image-36975\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-1024x576.jpg 1024w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-300x169.jpg 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-768x432.jpg 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-1536x864.jpg 1536w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-747x420.jpg 747w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-150x84.jpg 150w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-696x392.jpg 696w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302-1068x601.jpg 1068w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-11T075915.302.jpg 1920w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><figcaption class=\"wp-element-caption\">Imagem: Canva.<\/figcaption><\/figure>\n\n\n\n<p>A <strong>vasculite sist\u00eamica<\/strong> \u00e9 um tema que sempre aparece nas provas. Por isso, relembre as principais vasculites, suas classifica\u00e7\u00f5es e detalhes essenciais desse tema!<br><\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-o-que-e-vasculite\"><span class=\"ez-toc-section\" id=\"O_que_e_vasculite\"><\/span><strong>O que \u00e9 vasculite?<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Vasculite \u00e9 a <strong>inflama\u00e7\u00e3o e necrose do vaso sangu\u00edneo<\/strong>, que leva \u00e0 <strong>incapacidade de manter o fluxo sangu\u00edneo,<\/strong> resultando em <strong>perfura\u00e7\u00e3o, hemorragia, trombose e isquemia.<\/strong> As vasculites sist\u00eamicas frequentemente se manifestam com <strong>sintomas inespec\u00edficos,<\/strong> como perda de peso, fadiga e febre.<\/p>\n\n\n\n<p>Elas s\u00e3o classificadas de acordo com o <strong>tamanho do vaso<\/strong> que afetam: <strong>grandes, m\u00e9dios ou pequenos vasos.<\/strong><\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-vasculites-de-grandes-vasos\"><span class=\"ez-toc-section\" id=\"Vasculites_de_Grandes_Vasos\"><\/span><strong>Vasculites de Grandes Vasos<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Aqui, os destaques s\u00e3o a <strong>Arterite de Takayasu e a Arterite de C\u00e9lulas Gigantes.<\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Arterite de Takayasu<\/strong><\/li>\n<\/ul>\n\n\n\n<p>&nbsp;Conhecida como &#8220;<strong>doen\u00e7a sem pulso<\/strong>&#8220;, afeta predominantemente mulheres jovens, com idade m\u00e9dia de 25 anos. A <strong>etiologia \u00e9 desconhecida<\/strong>, mas a doen\u00e7a causa <strong>estenose<\/strong> de <strong>grandes vasos e aneurismas<\/strong>, principalmente nos vasos que saem da aorta.<\/p>\n\n\n\n<figure class=\"wp-block-image size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"835\" height=\"1024\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image-835x1024.jpeg\" alt=\"\t\nDescri\u00e7\u00e3o da circula\u00e7\u00e3o sangu\u00ednea na aorta, incluindo elementos como tronco braquiocef\u00e1lico, art\u00e9ria car\u00f3tida comum esquerda, art\u00e9ria subcl\u00e1via esquerda, aorta ascendente, arco a\u00f3rtico, aorta descendente, por\u00e7\u00e3o tor\u00e1cica e abdominal, al\u00e9m de art\u00e9rias principais.\" class=\"wp-image-36976\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image-835x1024.jpeg 835w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image-245x300.jpeg 245w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image-768x942.jpeg 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image-342x420.jpeg 342w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image-150x184.jpeg 150w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image-300x368.jpeg 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image-696x854.jpeg 696w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/image.jpeg 1054w\" sizes=\"auto, (max-width: 835px) 100vw, 835px\" \/><figcaption class=\"wp-element-caption\">Irriga\u00e7\u00e3o principal da aorta. Fonte: Acervo de Ilustra\u00e7\u00f5es do Grupo MedCof.<\/figcaption><\/figure>\n\n\n\n<p>A Arterite de Takayasu pode causar <strong>sintomas sist\u00eamicos<\/strong> (perda de peso, febre, mialgia), <strong>vasculares<\/strong> (claudica\u00e7\u00e3o intermitente em membros superiores e inferiores) e <strong>neurol\u00f3gicos<\/strong> (cefaleia, vertigem, AVC). Uma caracter\u00edstica \u00e9 a <strong>diferen\u00e7a de pulsos e press\u00e3o arterial entre os membros.<\/strong><\/p>\n\n\n\n<p>&nbsp;O diagn\u00f3stico \u00e9 feito pela <strong>angiografia<\/strong>, que&nbsp; \u00e9 o <strong>padr\u00e3o-ouro<\/strong>. Os crit\u00e9rios de <strong>1990 do ACR<\/strong> incluem a <strong>presen\u00e7a de 3 dos 6 pontos:<\/strong>&nbsp;<\/p>\n\n\n\n<figure class=\"wp-block-table\"><table class=\"has-fixed-layout\"><tbody><tr><td>Sexo feminino&nbsp;<\/td><td>+1<\/td><\/tr><tr><td>Angina ou dor isqu\u00eamica card\u00edaca&nbsp;<\/td><td>+2<\/td><\/tr><tr><td>Claudica\u00e7\u00e3o de bra\u00e7os ou pernas&nbsp;<\/td><td>+2<\/td><\/tr><tr><td>Sopro vascular&nbsp;<\/td><td>+2<\/td><\/tr><tr><td>Pulso reduzido na extremidade superior&nbsp;<\/td><td>+2<\/td><\/tr><tr><td>Art\u00e9ria car\u00f3tida com anormalidade&nbsp;<\/td><td>+2<\/td><\/tr><tr><td>Diferen\u00e7a de PA entre MMSS &gt; 20 mmHg<\/td><td>+1<\/td><\/tr><\/tbody><\/table><\/figure>\n\n\n\n<p>O tratamento \u00e9 feito por meio de <strong>glicocortic\u00f3ides<\/strong>, que s\u00e3o a primeira linha. Imunossupressores como <strong>Micofenolato de Mofetil (MMF), Azatioprina (AZA), Metotrexato (MTX), Leflunomida e Ciclosporina<\/strong> s\u00e3o usados para poupar o corticoide ou em casos mais graves. Em casos refrat\u00e1rios, imunobiol\u00f3gicos como <strong>Tocilizumabe<\/strong> e <strong>Infliximabe<\/strong> s\u00e3o op\u00e7\u00f5es.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-arterite-de-celulas-gigantes-acg\"><span class=\"ez-toc-section\" id=\"Arterite_de_Celulas_Gigantes_ACG\"><\/span><strong>Arterite de C\u00e9lulas Gigantes (ACG)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Principal causa de <strong>febre de origem indeterminada em idosos.<\/strong> \u00c9 mais comum em mulheres (3:1) acima de 50 anos e est\u00e1 frequentemente associada \u00e0 <strong>Polimialgia Reum\u00e1tica<\/strong>.<\/p>\n\n\n\n<p>&nbsp;&nbsp;&nbsp;Falando em cl\u00ednica, a <strong>cefaleia<\/strong> \u00e9 o sintoma mais comum, mas tamb\u00e9m pode causar <strong>altera\u00e7\u00f5es visuais graves<\/strong>. A <strong>claudica\u00e7\u00e3o de mand\u00edbula<\/strong> \u00e9 um sintoma mais espec\u00edfico.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXegTdfSzaPT2dqZ-bxsKWy2CqGbwQ1SHEwZiWzyJCdTSGqZYiViwkgEERKW1dxX0QQl914-gKPsZGdyCZN4cNa48SFOjeTy64U6sshdBi2G56WyRTzXacYOk6rCaaWmmothj3a06g?key=3ZcYlYMB7llpaefBRisErQ\" alt=\"\"\/><figcaption class=\"wp-element-caption\">Espessamento temporal como manifesta\u00e7\u00f5es das c\u00e9lulas Gigantes. Fonte: ACR &#8211; American College of Rheumatology.\u00a0<\/figcaption><\/figure>\n\n\n\n<p>Nesse caso, o diagn\u00f3stico \u00e9 feito por meio da <strong>bi\u00f3psia da art\u00e9ria temporal<\/strong>, embora haja risco de falso negativo. O <strong>aumento de PCR e VHS<\/strong> sugere a doen\u00e7a.<\/p>\n\n\n\n<p><strong>Glicocortic\u00f3ides s\u00e3o a base do tratamento<\/strong>. A dosagem \u00e9 de 40 mg\/dia para casos n\u00e3o complicados e 60 mg\/dia para aortite ou acometimento oft\u00e1lmico. O <strong>Tocilizumabe<\/strong> \u00e9 um imunobiol\u00f3gico que tem ganhado destaque. <strong>\u00c9 importante n\u00e3o atrasar o tratamento para fazer a bi\u00f3psia.<\/strong><\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-vasculites-de-medios-vasos\"><span class=\"ez-toc-section\" id=\"Vasculites_de_Medios_Vasos\"><\/span><strong>Vasculites de M\u00e9dios Vasos<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>A <strong>Poliarterite Nodosa (PAN)<\/strong> \u00e9 a principal representante.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-poliarterite-nodosa-pan\"><span class=\"ez-toc-section\" id=\"Poliarterite_Nodosa_PAN\"><\/span><strong>Poliarterite Nodosa (PAN)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Uma vasculite necrosante sist\u00eamica que afeta principalmente <strong>vasos viscerais, cut\u00e2neos, musculares e de nervos perif\u00e9ricos. <\/strong>\u00c9 uma doen\u00e7a <strong>rara<\/strong>, com pico de incid\u00eancia entre a 5\u00aa e 6\u00aa d\u00e9cadas de vida.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXfQ0yDx2oJLL4nKbtCL59euVh9VuoAGVd9CN6TrTDYgrA3WMN0X2TXWZCfded9WrTmMpS9Ft0a80cJZJXHz91Cu1VF52-i-rMeN92cthCuDuB7QdItNm44HOYG3t19Kl1uqTIsHZA?key=3ZcYlYMB7llpaefBRisErQ\" alt=\"\"\/><figcaption class=\"wp-element-caption\">Acometimento dos nervos perif\u00e9ricos, manifestando-se como m\u00e3o ca\u00edda. Fonte: American College of Rheumatology.\u00a0<\/figcaption><\/figure>\n\n\n\n<p>Podemos lembrar que &#8220;<strong>PAN poupa o pulm\u00e3o<\/strong>&#8220;. Os sintomas incluem <strong>mononeurite m\u00faltipla, livedo, n\u00f3dulos e necrose na pele<\/strong>. <strong>Dor testicular<\/strong>, geralmente unilateral, \u00e9 um sintoma t\u00edpico.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXfS8nrp8vDYBOnlnL3NgJN3eI_WLP7omdk7tyx0smkvYcKjjcA1FXZdGNmghPJoF3Dv4tlzMj0_QV--QZEBZJsAf8PvYlC-h2AcjT5MFQA877hZ1K_6955wxnrjQMnD6pvqEj1GsQ?key=3ZcYlYMB7llpaefBRisErQ\" alt=\"\"\/><figcaption class=\"wp-element-caption\">P\u00farpuras em membros inferiores como manifesta\u00e7\u00e3o predominante da PAN nessa regi\u00e3o. Fonte: American College of Rheumatology.\u00a0<\/figcaption><\/figure>\n\n\n\n<p>O diagn\u00f3stico \u00e9 feito pela <strong>arteriografia<\/strong>, que mostra <strong>estenoses e microaneurismas<\/strong>. A bi\u00f3psia cut\u00e2nea pode revelar <strong>vasculite leucocitocl\u00e1stica<\/strong>. A exclus\u00e3o de v\u00edrus associados como hepatite B, C e HIV \u00e9 fundamental.<\/p>\n\n\n\n<p>A escolha do tratamento depende do <strong>Five Factor Score (FFS),<\/strong> que inclui <strong>insufici\u00eancia renal, protein\u00faria, envolvimento gastrointestinal, card\u00edaco e do SNC<\/strong>. Se FFS for zero, usa-se <strong>glicocorticoide isolado<\/strong>. Se FFS for maior ou igual a um, usa-se <strong>Ciclofosfamida<\/strong>.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-vasculites-de-pequenos-vasos\"><span class=\"ez-toc-section\" id=\"Vasculites_de_Pequenos_Vasos\"><\/span><strong>Vasculites de Pequenos Vasos<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Este grupo inclui as <strong>vasculites ANCA-associadas (GPA, GEPA, PAM) e a Crioglobulinemia.<\/strong><\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-vasculites-anca-associadas\"><span class=\"ez-toc-section\" id=\"Vasculites_ANCA-associadas\"><\/span><strong>Vasculites ANCA-associadas<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>Associadas ao anticorpo anticitoplasma de neutr\u00f3filos (ANCA).<\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-granulomatose-com-poliangiite-gpa\"><span class=\"ez-toc-section\" id=\"Granulomatose_com_Poliangiite_GPA\"><\/span><strong>Granulomatose com Poliangiite (GPA)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>&nbsp;Anteriormente conhecida como <strong>granulomatose de Wegener<\/strong>, \u00e9 a mais frequente das vasculites ANCA-associadas. \u00c9 tipicamente associada ao <strong>C-ANCA e ao Anti-PR3.<\/strong> O quadro cl\u00ednico \u00e9 conhecido como &#8220;<strong>pulm\u00e3o-rim<\/strong>&#8220;. Pacientes podem ter sintomas em vias a\u00e9reas superiores, como <strong>obstru\u00e7\u00e3o nasal, sinusite e estenose subgl\u00f3tica<\/strong>. O &#8220;nariz em sela&#8221; \u00e9 uma deformidade caracter\u00edstica.<\/p>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXfsAqlxfe01aJie44XO4oB_6kOoWelq2v49hhlOdSHGN-h70IdrsIbyVZ_J5Yhnl-TYPpvTdHjkd-pwQjaWolCP1S662pUkhwIaSTfMSkBxImMLFsoGOzyRkKk0_Qjl6NwhI6ZS?key=3ZcYlYMB7llpaefBRisErQ\" alt=\"\"\/><figcaption class=\"wp-element-caption\">Manifesta\u00e7\u00e3o do nariz em sela. Fonte: <a href=\"https:\/\/images.app.goo.gl\/AqoABfjxqeGRkehE7\">https:\/\/images.app.goo.gl\/AqoABfjxqeGRkehE7<\/a><\/figcaption><\/figure>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-granulomatose-eosinofilica-com-poliangiite-gepa\"><span class=\"ez-toc-section\" id=\"Granulomatose_Eosinofilica_com_Poliangiite_GEPA\"><\/span><strong>Granulomatose Eosinof\u00edlica com Poliangiite (GEPA)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>\u00a0Antes chamada de Doen\u00e7a de <strong>Churg-Strauss<\/strong>. A <strong>asma<\/strong> \u00e9 uma caracter\u00edstica definidora. O perfil laboratorial mostra <strong>P-ANCA e Anti-MPO.<\/strong> Manifesta\u00e7\u00f5es <strong>neurol\u00f3gicas<\/strong>, como a <strong>mononeurite m\u00faltipla<\/strong>, s\u00e3o comuns.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-poliangiite-microscopica-pam\"><span class=\"ez-toc-section\" id=\"Poliangiite_Microscopica_PAM\"><\/span><strong>Poliangiite Microsc\u00f3pica (PAM)<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>&nbsp;Predomina em <strong>homens por volta dos 50 anos<\/strong> e evolui com manifesta\u00e7\u00f5es de &#8220;<strong>pulm\u00e3o-rim<\/strong>&#8220;( \u00e9 a causa t\u00edpica da s\u00edndrome pulm\u00e3o-rim). O envolvimento renal predominante \u00e9 a <strong>glomerulonefrite rapidamente progressiva (GNRP<\/strong>). \u00c9 associada ao P-ANCA em 75% dos casos.<\/p>\n\n\n\n<p>O tratamento das doen\u00e7as ANCA-associadas \u00e9 feito com <strong>Ciclofosfamida ou Rituximabe<\/strong>, para indu\u00e7\u00e3o e manuten\u00e7\u00e3o. Em casos leves, <strong>Micofenolato de Mofetila e prednisona<\/strong>. Para GNRP ou hemorragia alveolar difusa (HAD), <strong>plasmaf\u00e9rese<\/strong> deve ser considerada. O <strong>Mepolizumabe<\/strong> (anti-IL-5) \u00e9 usado para GEPA.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-crioglobulinemia\"><span class=\"ez-toc-section\" id=\"Crioglobulinemia\"><\/span><strong>Crioglobulinemia<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h3>\n\n\n\n<p>&nbsp;\u00c9 uma vasculite rara, mais comum em <strong>mulheres entre a 4\u00aa e 5\u00aa d\u00e9cadas de vida.<\/strong> O gatilho imunol\u00f3gico mais conhecido \u00e9 o <strong>v\u00edrus da hepatite C (HCV).<\/strong><\/p>\n\n\n\n<p>&nbsp;&nbsp;Ela se caracteriza por <strong>p\u00farpuras em extremidades<\/strong> que n\u00e3o desaparecem \u00e0 digitopress\u00e3o.Para fazer o diagn\u00f3stico, \u00e9 essencial pesquisar o <strong>HCV<\/strong> e quantificar as <strong>crioglobulinas<\/strong>. O complemento costuma estar consumido e o fator reumatoide, positivo.<\/p>\n\n\n\n<figure class=\"wp-block-image is-resized\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXfRgkdzowEEIvCH1xJaFvqifh4U8YrpaNZixXCGyQf3RArUDpFalEmIivRGpPLaB684Vv3_Zq08e4yiv_1MLpe4LnKd_UxDLmCoMfYn_32cedD35a0s5wTrozJ4LSCQo1nLCT0toA?key=3ZcYlYMB7llpaefBRisErQ\" alt=\"\" style=\"width:496px;height:auto\"\/><figcaption class=\"wp-element-caption\">P\u00farpura em pavilh\u00e3o auricular.\u00a0 Fonte: Aries, P., Ullrich, S. &amp; Gross, W. A case of destructive Wegener\u2019s granulomatosis complicated by cytomegalovirus infection. Nat Rev Rheumatol 2, 511\u2013515 (2006).<\/figcaption><\/figure>\n\n\n\n<p>O tratamento varia conforme a gravidade: para casos leves associados ao HCV, terapia <strong>antiviral<\/strong> e <strong>glicocortic\u00f3ides<\/strong>. Casos moderados com acometimento de \u00f3rg\u00e3o-alvo s\u00e3o tratados com <strong>Rituximabe e glicocortic\u00f3ides<\/strong>. Para manifesta\u00e7\u00f5es graves como <strong>HAD<\/strong>, <strong>plasmaf\u00e9rese e ciclofosfamida<\/strong> s\u00e3o indicados.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"o-m\u00e9todo-que-te-aprova\"><span class=\"ez-toc-section\" id=\"O_metodo_que_te_aprova\"><\/span><strong>O m\u00e9todo que te aprova!<\/strong><span class=\"ez-toc-section-end\"><\/span><\/h2>\n\n\n\n<p>Quer alcan\u00e7ar a aprova\u00e7\u00e3o nas provas de resid\u00eancia m\u00e9dica? Ent\u00e3o seja um&nbsp;<a href=\"https:\/\/www.grupomedcof.com.br\/home\/\" target=\"_blank\" rel=\"noreferrer noopener\">MedCoffer<\/a>! Aqui te ajudaremos na busca da aprova\u00e7\u00e3o com conte\u00fados de qualidade e uma&nbsp;<a href=\"https:\/\/www.grupomedcof.com.br\/blog\/presenca-da-medcof-nas-aprovacoes-em-residencia-medica-no-brasil\/\" target=\"_blank\" rel=\"noreferrer noopener\">metodologia que j\u00e1 aprovou mais de 20 mil residentes no pa\u00eds!&nbsp;<\/a>Por fim, acesse o nosso<a href=\"https:\/\/www.youtube.com\/@GrupoMedcof\/featured\" target=\"_blank\" rel=\"noreferrer noopener\">&nbsp;<strong>canal do youtube&nbsp;<\/strong><\/a>para ver o nosso material.&nbsp;<\/p>\n\n\n\n<figure class=\"wp-block-embed is-type-video is-provider-youtube wp-block-embed-youtube wp-embed-aspect-16-9 wp-has-aspect-ratio\"><div class=\"wp-block-embed__wrapper\">\n<div class=\"youtube-embed\" data-video_id=\"EJmTEP1m1GE\"><iframe loading=\"lazy\" title=\"COFEXPRESS - Vasculites Sist\u00eamicas. Com Dr. Henrique Dalmolin\" width=\"696\" height=\"392\" src=\"https:\/\/www.youtube.com\/embed\/EJmTEP1m1GE?feature=oembed&#038;enablejsapi=1\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe><\/div>\n<\/div><\/figure>\n","protected":false},"excerpt":{"rendered":"<p>Conhe\u00e7a tipos, sintomas, diagn\u00f3stico e tratamentos das formas mais comuns, dos grandes aos pequenos vasos da vasculite.<\/p>\n","protected":false},"author":21,"featured_media":36975,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[101],"tags":[3073,3070,3068,3069,3071,3072],"ppma_author":[3617],"class_list":{"0":"post-36971","1":"post","2":"type-post","3":"status-publish","4":"format-standard","5":"has-post-thumbnail","7":"category-reumatologia","8":"tag-anca","9":"tag-arterite","10":"tag-vasculite","11":"tag-vasculite-de-grandes-vasos","12":"tag-vasculite-de-medios-vasos","13":"tag-vasculite-de-pequenos-vasos"},"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v24.3 (Yoast SEO v27.4) - 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