{"id":37436,"date":"2025-08-29T15:30:00","date_gmt":"2025-08-29T18:30:00","guid":{"rendered":"https:\/\/www.grupomedcof.com.br\/blog\/?p=37436"},"modified":"2026-04-24T16:40:01","modified_gmt":"2026-04-24T19:40:01","slug":"anemia-hemolitica-adquirida","status":"publish","type":"post","link":"https:\/\/www.grupomedcof.com.br\/blog\/anemia-hemolitica-adquirida\/","title":{"rendered":"Anemia Hemol\u00edtica Adquirida: fisiologia, classifica\u00e7\u00f5es e mais!"},"content":{"rendered":"\n<figure class=\"wp-block-image size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"576\" src=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-1024x576.jpg\" alt=\"\" class=\"wp-image-37440\" srcset=\"https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-1024x576.jpg 1024w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-300x169.jpg 300w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-768x432.jpg 768w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-1536x864.jpg 1536w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-747x420.jpg 747w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-150x84.jpg 150w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-696x392.jpg 696w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790-1068x601.jpg 1068w, https:\/\/www.grupomedcof.com.br\/blog\/wp-content\/uploads\/2025\/08\/Blog-MedCof-2025-08-28T134720.790.jpg 1920w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n\n\n\n<p class=\"wp-block-paragraph\">A <strong>anemia hemol\u00edtica adquirid<\/strong>a caracteriza-se como a condi\u00e7\u00e3o hematol\u00f3gica em que <strong>fatores externos ao organismo eliminam os gl\u00f3bulos vermelhos<\/strong> antes do tempo normal.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-fisiologia-da-hemacia-nbsp\"><strong>Fisiologia da hem\u00e1cia&nbsp;<\/strong><\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">A <strong>eritropoiese<\/strong>, processo de forma\u00e7\u00e3o dos gl\u00f3bulos vermelhos, inicia-se na medula \u00f3ssea, presente nos ossos longos de adultos. Quando a matura\u00e7\u00e3o das hem\u00e1cias \u00e9 alcan\u00e7ada, elas s\u00e3o <strong>liberadas na circula\u00e7\u00e3o perif\u00e9rica<\/strong> com uma pequena porcentagem de reticul\u00f3citos. Em condi\u00e7\u00f5es normais, a hem\u00e1cia tem uma vida \u00fatil de cerca de <strong>120 dias<\/strong>, sendo posteriormente fagocitada por macr\u00f3fagos no ba\u00e7o. <\/p>\n\n\n\n<p class=\"wp-block-paragraph\">O organismo <strong>recicla<\/strong> o conte\u00fado interno das hem\u00e1cias: a transferrina <strong>transporta<\/strong> o ferro, enquanto o f\u00edgado <strong>recebe<\/strong> a bilirrubina indireta (produto da destrui\u00e7\u00e3o) para excre\u00e7\u00e3o. <\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Quando os n\u00edveis de reticul\u00f3citos superam 2% ou 100 mil em um quadro de anemia, os m\u00e9dicos <strong>classificam<\/strong> a condi\u00e7\u00e3o como anemia hiperproliferativa. As principais causas de anemias hiperproliferativas s\u00e3o as anemias <strong>hemol\u00edticas e o sangramento agudo<\/strong>.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-quais-as-provas-de-hemolise-nbsp\"><strong>Quais as provas de hem\u00f3lise?&nbsp;<\/strong><\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">As provas de hem\u00f3lise s\u00e3o os exames laboratoriais que indicam a destrui\u00e7\u00e3o acelerada de hem\u00e1cias. Os principais achados s\u00e3o:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Reticulocitose:&nbsp;<\/strong>A medula \u00f3ssea saud\u00e1vel, em resposta \u00e0 redu\u00e7\u00e3o da massa eritr\u00f3ide, <strong>aumenta a produ\u00e7\u00e3o de gl\u00f3bulos vermelhos,<\/strong> liberando-os de <strong>forma imatura<\/strong> na forma de reticul\u00f3citos. A reticulocitose \u00e9 definida como mais de 2% ou 100 mil reticul\u00f3citos.<\/li>\n\n\n\n<li><strong>Aumento de DHL:<\/strong> A les\u00e3o da membrana das hem\u00e1cias provoca o <strong>aumento da enzima desidrogenase l\u00e1tica<\/strong> (DHL).<\/li>\n\n\n\n<li><strong>Consumo de Haptoglobina:<\/strong> &nbsp;Para evitar les\u00f5es endoteliais, a <strong>haptoglobina<\/strong> se liga \u00e0 <strong>hemoglobina livre no plasma<\/strong>. Isso resulta no consumo e redu\u00e7\u00e3o dos n\u00edveis de haptoglobina.<\/li>\n\n\n\n<li><strong>Aumento de Bilirrubina Indireta:<\/strong> A bilirrubina indireta, um componente da hem\u00e1cia, aumenta no plasma devido \u00e0 <strong>destrui\u00e7\u00e3o celular<\/strong>.<\/li>\n\n\n\n<li><strong>Anemia Hemol\u00edtica Autoimune (AHAI):<\/strong> A AHAI \u00e9 uma anemia hemol\u00edtica adquirida que ocorre devido \u00e0 <strong>forma\u00e7\u00e3o de autoanticorpos contra os gl\u00f3bulos vermelhos.<\/strong> Os exames apresentam provas de hem\u00f3lise positivas, e o teste de Coombs Direto positivo confirma o diagn\u00f3stico. <strong>Anticorpos da classe IgG causam cerca de 75-90% dos casos, embora IgM e IgA tamb\u00e9m possam participar do processo.<\/strong><\/li>\n<\/ul>\n\n\n\n<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXeCgJRv5BK2dhT4OmmvIWU0w2NVp9gpoVhPDgXelPTDC2XyUjFl35Vm55duCR7qMhOS4Vw2zWi32YcUY-klNZW5FlqgaHjF3Hw74F9d1t9R3YPmA_DX_PBa9-SUMC6VnMn0MQQ8?key=1ewlLM3gXyQhJ-o82FQ1rw\" alt=\"\"\/><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-quais-as-classificacoes-para-a-ahai-nbsp-nbsp\"><strong>Quais as classifica\u00e7\u00f5es para a AHAI?&nbsp;&nbsp;<\/strong><\/h2>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-ahai-quente\"><strong>AHAI Quente<\/strong><\/h3>\n\n\n\n<p class=\"wp-block-paragraph\">\u00a0\u00c9 o <strong>tipo mais comum<\/strong>. Os autoanticorpos da classe IgG <strong>aderem<\/strong> aos eritr\u00f3citos, e os macr\u00f3fagos no ba\u00e7o <strong>destroem<\/strong> essas c\u00e9lulas (hem\u00f3lise extravascular). Temperaturas entre 37\u00b0C e 40\u00b0C <strong>intensificam<\/strong> esse processo. Na hematoscopia, o analista <strong>observa<\/strong> esfer\u00f3citos \u2014 hem\u00e1cias que perderam a palidez central.<\/p>\n\n\n\n<figure class=\"wp-block-image is-resized\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXcLdPCyuvZ4gzbJwOvScLXXymlkJL5qoujxHNP30XMm6_Am9z0DSUqDC2kwjWnnorzuPuLhtYHLTMo2SwWjbeqdG6WQY0JI6ZD6UBlvBgWFax5Wf0rN7ghXZDGqAA49QVr9K8oA?key=1ewlLM3gXyQhJ-o82FQ1rw\" alt=\"\" style=\"width:524px;height:auto\"\/><figcaption class=\"wp-element-caption\">L\u00e2mina hematol\u00f3gica com esfer\u00f3citos. Fonte: <a href=\"https:\/\/images.app.goo.gl\/5gorqPRR7SzQUYf89\">https:\/\/images.app.goo.gl\/5gorqPRR7SzQUYf89<\/a>&nbsp;<\/figcaption><\/figure>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-ahai-fria\"><strong>AHAI Fria<\/strong><\/h3>\n\n\n\n<p class=\"wp-block-paragraph\">Caracterizada por <strong>autoanticorpos da classe IgM que se ligam aos eritr\u00f3citos<\/strong> e ativam a <strong>via alternativa do sistema complementar<\/strong>. Essa ativa\u00e7\u00e3o leva \u00e0 forma\u00e7\u00e3o do complexo de ataque \u00e0 membrana <strong>(MAC)<\/strong>, que causa a <strong>lise celular<\/strong> (hem\u00f3lise intravascular). Este tipo est\u00e1 mais relacionado a <strong>infec\u00e7\u00f5es e neoplasias<\/strong>.<\/p>\n\n\n\n<figure class=\"wp-block-image is-resized\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXcH5eoSHe1xe0HJlJEjx2kcaP9pK_0Z0Rz9LEtoBcewcawTUIvlmrsUaOdrW8f402SxnI60ML98NcD5HB8iAIp-EvuZYCiJokXHv6DetR6fsjXFMmUkZtm4FQM0UIut3NhwBoPvqg?key=1ewlLM3gXyQhJ-o82FQ1rw\" alt=\"\" style=\"width:666px;height:auto\"\/><figcaption class=\"wp-element-caption\">Fisiologia da anemia hemol\u00edtica adquirida autoimune. Fonte: <a href=\"http:\/\/scielo.sld.cu\/scielo.php?script=sci_arttext&amp;pid=S0864-02892022000400009\">http:\/\/scielo.sld.cu\/scielo.php?script=sci_arttext&amp;pid=S0864-02892022000400009<\/a>&nbsp;<\/figcaption><\/figure>\n\n\n\n<p class=\"wp-block-paragraph\">A AHAI pode ser secund\u00e1ria a outras condi\u00e7\u00f5es, como <strong>neoplasias<\/strong> (especialmente leucemia linfoc\u00edtica cr\u00f4nica), <strong>doen\u00e7as autoimunes<\/strong> (l\u00fapus eritematoso sist\u00eamico), <strong>infec\u00e7\u00f5es<\/strong> (EBV, Mycoplasma) ou <strong>drogas<\/strong>. O tratamento de primeira linha \u00e9 o uso de <strong>corticoides <\/strong>na dose de 1-2~mg\/kg\/dia.<\/p>\n\n\n\n<h3 class=\"wp-block-heading\" id=\"h-hemoglobinuria-paroxistica-noturna-hpn\"><strong>Hemoglobin\u00faria Parox\u00edstica Noturna (HPN)<\/strong><\/h3>\n\n\n\n<p class=\"wp-block-paragraph\">A HPN \u00e9 uma anemia <strong>hemol\u00edtica cr\u00f4nica adquirida<\/strong>, mas n\u00e3o imune. \u00c9 causada por uma <strong>muta\u00e7\u00e3o no gene PIG A,<\/strong> que \u00e9 respons\u00e1vel pela codifica\u00e7\u00e3o de enzimas de membrana que ancoram os <strong>marcadores CD55 e CD59<\/strong>. O CD55 previne a forma\u00e7\u00e3o da mol\u00e9cula C3 <strong>convertase<\/strong>, enquanto o CD59 <strong>bloqueia a liga\u00e7\u00e3o do C9<\/strong>, impedindo a forma\u00e7\u00e3o do complexo de ataque \u00e0 membrana. Na HPN, a defici\u00eancia desses marcadores faz com que o sistema complemento <strong>n\u00e3o reconhe\u00e7a as hem\u00e1cias como pr\u00f3prias<\/strong>, desencadeando uma <strong>hem\u00f3lise intravascular maci\u00e7a<\/strong>.<\/p>\n\n\n\n<figure class=\"wp-block-image is-resized\"><img decoding=\"async\" src=\"https:\/\/lh7-rt.googleusercontent.com\/docsz\/AD_4nXcMkrQ5l8D11ihOWTfzlYZYy_9Hx08bvJGwiPLeKE6Jx2W5XA8Iyg1sW7DDoI7TkLwu4GRIDPbFGW3Mz0MhMqIrIlDv0nET7xJb8JPInOLSZYK3UELgJGLYITXXSNEcyVzIaGf2cA?key=1ewlLM3gXyQhJ-o82FQ1rw\" alt=\"\" style=\"width:473px;height:auto\"\/><figcaption class=\"wp-element-caption\">Fisiopatologia da HPN. Fonte: <a href=\"https:\/\/doi.org\/10.1590\/S0104-42302010000200022\">https:\/\/doi.org\/10.1590\/S0104-42302010000200022<\/a>&nbsp;<\/figcaption><\/figure>\n\n\n\n<p class=\"wp-block-paragraph\">O m\u00e9dico deve <strong>considerar o diagn\u00f3stico<\/strong> de HPN em pacientes que apresentem anemia hemol\u00edtica intravascular, tromboses e citopenias. As provas laboratoriais incluem anemia com <strong>reticulocitose<\/strong>, <strong>aumento de DHL e redu\u00e7\u00e3o da haptoglobina<\/strong>. O teste de Coombs Direto \u00e9 negativo. O padr\u00e3o-ouro para o diagn\u00f3stico \u00e9 a <strong>citometria de fluxo.<\/strong> O tratamento de primeira linha para HPN \u00e9 o <strong>Eculizumab<\/strong>, um anticorpo monoclonal que impede a clivagem do C5, evitando a forma\u00e7\u00e3o do complexo de ataque \u00e0 membrana. <strong>O transplante de medula \u00f3ssea \u00e9 reservado para casos refrat\u00e1rios.<\/strong><\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-quais-outras-anemias-hemoliticas-podem-ser-adquiridas\"><strong>Quais outras Anemias Hemol\u00edticas podem ser adquiridas?<\/strong><\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Existem tamb\u00e9m outras etiologias adquiridas, como:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Mec\u00e2nicas: Causadas por <strong>pr\u00f3teses valvares.<\/strong><\/li>\n\n\n\n<li>Microangiopatias: Como a <strong>P\u00farpura Trombocitop\u00eanica Tromb\u00f3tica<\/strong> (PTT), a <strong>S\u00edndrome Hemol\u00edtico-Ur\u00eamica<\/strong> (SHU) e a <strong>S\u00edndrome HELLP.<\/strong><\/li>\n\n\n\n<li>Infec\u00e7\u00f5es: Como a <strong>mal\u00e1ria<\/strong>.<\/li>\n\n\n\n<li>Anemias Induzidas por Drogas: Mais de 150 medicamentos, incluindo metildopa e penicilinas, podem <strong>induzir fen\u00f4menos imunol\u00f3gicos<\/strong>.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"o-m\u00e9todo-que-te-aprova\"><strong>O m\u00e9todo que te aprova!<\/strong><\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Quer alcan\u00e7ar a aprova\u00e7\u00e3o nas provas de resid\u00eancia m\u00e9dica? Ent\u00e3o seja um&nbsp;<a href=\"https:\/\/www.grupomedcof.com.br\/home\/\" target=\"_blank\" rel=\"noreferrer noopener\">MedCofer<\/a>! Aqui te ajudaremos na busca da aprova\u00e7\u00e3o com conte\u00fados de qualidade e uma&nbsp;<a href=\"https:\/\/www.grupomedcof.com.br\/blog\/presenca-da-medcof-nas-aprovacoes-em-residencia-medica-no-brasil\/\" target=\"_blank\" rel=\"noreferrer noopener\">metodologia que j\u00e1 aprovou mais de 20 mil residentes no pa\u00eds!&nbsp;<\/a>Por fim, acesse o nosso<a href=\"https:\/\/www.youtube.com\/@GrupoMedcof\/featured\" target=\"_blank\" rel=\"noreferrer noopener\">&nbsp;<strong>canal do youtube&nbsp;<\/strong><\/a>para ver o nosso material.<\/p>\n\n\n\n<figure class=\"wp-block-embed is-type-video is-provider-youtube wp-block-embed-youtube wp-embed-aspect-16-9 wp-has-aspect-ratio\"><div class=\"wp-block-embed__wrapper\">\n<div class=\"youtube-embed\" data-video_id=\"1rsuBaSAdxI\"><iframe loading=\"lazy\" title=\"COFEXPRESS - Anemias hemol\u00edticas adquiridas. Com Dra. Carolina Perrone\" width=\"696\" height=\"392\" src=\"https:\/\/www.youtube.com\/embed\/1rsuBaSAdxI?feature=oembed&#038;enablejsapi=1\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe><\/div>\n<\/div><\/figure>\n","protected":false},"excerpt":{"rendered":"<p>A anemia hemol\u00edtica adquirida \u00e9 caracterizada pela destrui\u00e7\u00e3o precoce das hem\u00e1cias, podendo estar associada a doen\u00e7as autoimunes, infec\u00e7\u00f5es ou medicamentos.<\/p>\n","protected":false},"author":21,"featured_media":37440,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[2600],"tags":[3725],"ppma_author":[3617],"class_list":["post-37436","post","type-post","status-publish","format-standard","has-post-thumbnail","category-hematologia","tag-anemia-hemolitica-adquirida"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.8 (Yoast SEO v27.8) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Anemia Hemol\u00edtica Adquirida: Fisiologia e Classifica\u00e7\u00e3o | Medcof<\/title>\n<meta name=\"description\" content=\"A anemia hemol\u00edtica adquirida \u00e9 a destrui\u00e7\u00e3o precoce das hem\u00e1cias, podendo estar associada a doen\u00e7as autoimunes, infec\u00e7\u00f5es ou medicamentos.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, 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